Idiopathische pulmonale fibrose: nieuwe inzichten

• Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive lung disease of unknown cause.
• IPF has a poor prognosis with a mean survival of 2 to 5 years after diagnosis.
• The diagnostic process is often complex and demands a multidisciplinary approach.
• To date, the only curative therapy available is lung transplant.
• New insights into the pathogenesis of IPF have brought about changes in standard treatment strategies.
• New drugs have recently become available and have been shown to slow down the decline in pulmonary function considerably and improve survival.

Conflict of interest and financial support: ICMJE forms provided by the authors are available online along with the full text of this article.